GenPhenia

Step 1

Clinical setting

We begin with a real clinical scenario.

The case

A 16-year-old boy with delayed puberty and low reproductive hormone signals.

Benchmark

On the Mayo Clinic rare-disease dataset, GenPhenia outperforms Phen2Gene, PCAN, CADA, and PPAR (Mayo Clinic) across Top-1, Top-10, and Top-50 retrieval cutoffs.

Top-1 0.61Top-10 0.80Top-50 0.86

Benchmark comparison

Mayo Clinic rare-disease dataset

Mayo Clinic rare-disease datasetGrouped barplot comparing Phen2Gene, PCAN, CADA, PPAR (Mayo Clinic), and GenPhenia across Top-1, Top-10, and Top-50.% solved cases00.20.40.60.810.010.020.040.110.61Top-10.040.110.130.270.80Top-100.090.290.330.490.86Top-50
Phen2Gene
PCAN
CADA
PPAR (Mayo Clinic)
GenPhenia
PAPER

Clinical record

Patient

Age: 16 years

Sex: male

Clinical diagnosis: hypogonadotropic hypogonadism

History

Presenting feature: delayed puberty

Prior findings: cryptorchidism, microorchidism, micropenis

Biochemical record

Decreased FSH

Decreased LH

Decreased testosterone

Delayed puberty
Cryptorchidism
Micropenis
Decreased serum testosterone concentration

Step 1

Delayed puberty
Cryptorchidism
Micropenis
Decreased testosterone
HP:0000823
HP:0000028
HP:0000054
HP:0040171

Entering phenotype data

Natural language

HPO identifier

begin the phenotype

Step 1
Search one symptom at a time
HPO search

Try delayed puberty, cryptorchidism, micropenis, or decreased serum testosterone concentration.

HPO websiteDelayed puberty: HP:0000823
Press enter to add the highlighted symptom.0 symptoms selected
Loading the HPO symptom list.

Step 2

Now the differential diagnosis starts refining the phenotype.

Example question

Step 2
Differential diagnosis

Analyzing symptoms

GenPhenia is selecting the next question that best reduces the differential.

Compatible diseases

How it works

Before answer

Compatible diseases

After answer

Waiting for your answer

What follows

This step can repeat until the phenotype is informative enough.

Step 3

As you scroll, GenPhenia replays the path so far: clinical description, HPO encoding, differential refinement, and gene prioritization.

Step 4

Review the clinical record after the model run.

Phenotype graph

Explore the graph to see the clinical picture in perspective.

Observed findings stay visible while related follow-up terms remain anchored in context.

3 observedFollow-up in context
Phenotype
Delayed puberty
Decreased testicular size
Micropenis
Cryptorchidism
Low testosterone
Low LH
Low FSH
Observed
Follow-up
Ancestor

Get the most out of GenPhenia

More phenotypes and more specific phenotypes improve GenPhenia's output.

Mean HPO depth
9+
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1
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9
10+
Phenotype count
GenPhenia works better here
Current clinical picture

Click to add a phenotype and see how your clinical picture changes.

No HPO symptom match.
Loading the HPO symptom list.

Conclusion